Clinical case: Gorlin Goltz associated with Imperfect Osteogenesis

Abstract

The keratocystic odontogenic tumors are locally aggressive benign tumors that occur in the maxilla and mandible with a high rate of recurrence. These tumors usually present in a unique way, mainly in the mandibular angle. In certain occasions these tumors are associated with syndromes such as Gorlin Goltz. In which multiple keratocysts are observed in the jaws. In this article we present the case of a patient with multiple keratocysts tumors which also presents imperfect osteogenesis. A literature review was conducted to determine an association between osteogenesis imperfecta and multiple keratocysts tumors.